Congenital Hyperinsulinism Due to Hnf4a Deficiency, is also known as hyperinsulinemic hypoglycemia due to hnf4a deficiency. An important gene associated with Congenital Hyperinsulinism Due to Hnf4a Deficiency is HNF4A (Hepatocyte Nuclear Factor 4 Alpha). Affiliated tissues include pancreatic islet, and related phenotypes are hyperhidrosis and tremor