Congenital Factor Xiii Deficiency, also known as fibrin-stabilizing factor deficiency, is related to factor xiii deficiency and factor xiii, a subunit, deficiency of. An important gene associated with Congenital Factor Xiii Deficiency is F13A1 (Coagulation Factor XIII A Chain), and among its related pathways/superpathways are Response to elevated platelet cytosolic Ca2+ and Collagen chain trimerization. The drugs Benzocaine and Tannic acid have been mentioned in the context of this disorder. Affiliated tissues include myeloid and liver, and related phenotypes are abnormal umbilical stump bleeding and reduced factor xiii activity