Congenital Plasminogen Activator Inhibitor Type 1 Deficiency, also known as congenital pai-1 deficiency, is related to plasminogen activator inhibitor-1 deficiency and complete plasminogen activator inhibitor 1 deficiency. An important gene associated with Congenital Plasminogen Activator Inhibitor Type 1 Deficiency is SERPINE1 (Serpin Family E Member 1). Affiliated tissues include endothelial and heart, and related phenotypes are decreased level of plasminogen and persistent bleeding after trauma