Cholangitis, Primary Sclerosing (PSC)

Cholangitis, Primary Sclerosing(来自ICD-11)
别称:
Primary Sclerosing Cholangitis
Psc
Cholangitis, Sclerosing
Sclerosing Cholangitis
Psc - [primary Sclerosing Cholangitis]
Cholangitis Primary Sclerosing
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Basic Information
Medical Symptom
Gene & Mutation
Related Drugs
Disease Model
References Literature
Cholangitis, Primary Sclerosing, also known as primary sclerosing cholangitis, is related to autoimmune pancreatitis and choledocholithiasis, and has symptoms including icterus An important gene associated with Cholangitis, Primary Sclerosing is SEMA4D (Semaphorin 4D), and among its related pathways/superpathways are Defensins and Response of Mtb to phagocytosis. The drugs Bezafibrate and Simvastatin have been mentioned in the context of this disorder. Affiliated tissues include liver and small intestine, and related phenotypes are autoimmunity and cholestasis
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相关ID:
MESH:D015209
ICD11:857962451

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参考文献
MALACARDS
--
Child
<1/1000000
81
988
6

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