Childhood Type Dermatomyositis

Alias:
Juvenile Dermatomyositis
Juvenile Dm
Dermatomyositis, Childhood Type
Childhood Dermatomyositis
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Basic Information
Medical Symptom
Gene & Mutation
Related Drugs
Disease Model
References Literature
Childhood Type Dermatomyositis, also known as juvenile dermatomyositis, is related to raynaud disease and lupus erythematosus. An important gene associated with Childhood Type Dermatomyositis is MORC3 (MORC Family CW-Type Zinc Finger 3), and among its related pathways/superpathways are Antiviral mechanism by IFN-stimulated genes and Cytokine Signaling in Immune system. The drugs Abatacept and Vaccines have been mentioned in the context of this disorder. Affiliated tissues include skin and skeletal muscle, and related phenotypes are muscle weakness and fatigue
Related ID:
MESH:D003882
ICD11:1428089375

Basic Information

Inheritance
Age of Onset
Prevalence
Related Gene
Related Mouse Models
Reference
MALACARDS
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Infant
1-9/1000000
25
230
--

Medical Symptom

#
Categorization
Description
HPO Frequency
Orphanet Frequency
HPO Source Accession
No data available

Gene & Mutation

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Gene
Function
Score
Mutations
No data available

Related Drugs

Name
CAS Number
Status
Phase
No data available

Disease Model

Category
Name
MGI
Related Gene
Strain of Origin
Publications
No data available

References Literature

Title
PMID
Journal
Year
IF
No Data Found!
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