Blastic Plasmacytoid Dendritic Cell Neoplasm (BPDCN)

Alias:
Blastic Nk-Cell Lymphoma
Cd4+/cd56+ Hematodermic Neoplasm
Bpdcn
Agranular Cd4+ Cd56+ Hematodermic Neoplasm/tumor
Agranular Cd4+ Natural Killer Cell Leukemia
Agranular Cd4+/cd56+ Haematodermic Neoplasm
Lymphoblastoid Variant of Nk-Cell Lymphoma
Blastic Natural Killer Leukemia/lymphoma
Natural Killer Cell Leukemia/lymphoma
Blastic Nk-Cell Leukaemia/​lymphoma
Monomorphic Nk-Cell Lymphoma
Agranular Cd4+ Nk Leukaemia
Favorite
Basic Information
Medical Symptom
Gene & Mutation
Related Drugs
Disease Model
References Literature
Blastic Plasmacytoid Dendritic Cell Neoplasm, also known as blastic nk-cell lymphoma, is related to hematologic cancer and leukemia, acute monocytic. An important gene associated with Blastic Plasmacytoid Dendritic Cell Neoplasm is IL3RA (Interleukin 3 Receptor Subunit Alpha), and among its related pathways/superpathways are Innate Immune System and NF-kappaB Signaling. The drugs Cytarabine and Vincristine have been mentioned in the context of this disorder. Affiliated tissues include myeloid and bone marrow, and related phenotypes are immune system and hematopoietic system
Related ID:
ICD11:783045723

Basic Information

Inheritance
Age of Onset
Prevalence
Related Gene
Related Mouse Models
Reference
MALACARDS
--
Elderly
1-5/10000
20
173
--

Medical Symptom

#
Categorization
Description
HPO Frequency
Orphanet Frequency
HPO Source Accession
No data available

Gene & Mutation

#
Gene
Function
Score
Mutations
No data available

Related Drugs

Name
CAS Number
Status
Phase
No data available

Disease Model

Category
Name
MGI
Related Gene
Strain of Origin
Publications
No data available

References Literature

Title
PMID
Journal
Year
IF
No Data Found!
Wechat
Comparison
Al agent
Tutorials
Back to top