B-Cell Expansion with Nfkb and T-Cell Anergy (BENTA)

B-Cell Expansion with Nfkb and T-Cell Anergy(来自ICD-11)
别称:
Benta Disease
B-Cell Expansion with Nf-Kb and T-Cell Anergy Disease
Benta
Persistent Polyclonal B-Cell Lymphocytosis
Lymphocytosis
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Medical Symptom
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References Literature
B-Cell Expansion with Nfkb and T-Cell Anergy, also known as benta disease, is related to panniculitis and burkitt lymphoma. An important gene associated with B-Cell Expansion with Nfkb and T-Cell Anergy is CARD11 (Caspase Recruitment Domain Family Member 11), and among its related pathways/superpathways are Innate Immune System and Signal Transduction. The drugs Ofatumumab and Fludarabine have been mentioned in the context of this disorder. Affiliated tissues include b cells and spleen, and related phenotypes are splenomegaly and recurrent infections
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MALACARDS
AD
Infant
<1/1000000
18
201
16

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