Anti-Neutrophil Cytoplasmic Antibody-Associated Vasculitis (AAV)

Alias:
Antineutrophil Cytoplasmic Antibody-Associated Vasculitis
Anca-Associated Vasculitis
Aav
Anca - [antineutrophil Cytoplasmic Antibodies] Associated Vasculitis
Anca [antineutrophil Cytoplasmic Antibodies] Positive Vasculitis
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Basic Information
Medical Symptom
Gene & Mutation
Related Drugs
Disease Model
References Literature
Anti-Neutrophil Cytoplasmic Antibody-Associated Vasculitis, also known as antineutrophil cytoplasmic antibody-associated vasculitis, is related to vasculitis and polyarteritis nodosa. An important gene associated with Anti-Neutrophil Cytoplasmic Antibody-Associated Vasculitis is PRTN3 (Proteinase 3). The drugs Cyclophosphamide and Azathioprine have been mentioned in the context of this disorder. Affiliated tissues include neutrophil and lung.
Related ID:
ICD11:1404622826

Basic Information

Inheritance
Age of Onset
Prevalence
Related Gene
Related Mouse Models
Reference
MALACARDS
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Unknown
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1
6
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Medical Symptom

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Categorization
Description
HPO Frequency
Orphanet Frequency
HPO Source Accession
No data available

Gene & Mutation

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Gene
Function
Score
Mutations
No data available

Related Drugs

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CAS Number
Status
Phase
No data available

Disease Model

Category
Name
MGI
Related Gene
Strain of Origin
Publications
No data available

References Literature

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PMID
Journal
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IF
No Data Found!
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