Amyotrophic Lateral Sclerosis, Juvenile, with Dementia, also known as juvenile amyotrophic lateral sclerosis with dementia, is related to parkinsonism and muscular atrophy. An important gene associated with Amyotrophic Lateral Sclerosis, Juvenile, with Dementia is SNCB (Synuclein Beta). Related phenotypes are dementia and distal amyotrophy