Agammaglobulinemia 10, Autosomal Dominant, is also known as agammaglobulinemia, autosomal dominant, due to spi1 defect. An important gene associated with Agammaglobulinemia 10, Autosomal Dominant is SPI1 (Spi-1 Proto-Oncogene). Affiliated tissues include b cells, and related phenotypes are recurrent respiratory infections and agammaglobulinemia